Congenital malignant rhabdoid tumor of the scalp

Alistair R M Cobb, Neil J Sebire, John Anderson, David Dunaway

Research output: Contribution to journalArticle (Academic Journal)

8 Citations (Scopus)

Abstract

BACKGROUND: Malignant rhabdoid tumors (MRT) are rare but aggressive tumors presenting in the pediatric population. First thought a variant of Wilms' tumor in the kidney, it is recognized as presenting at renal, central nervous system and other extra-renal primary sites. It is uniformly of very poor prognosis, however.

CASE REPORT AND DISCUSSION: We present a case of congenital MRT of the scalp, which we believe to be the first described at this site. The clinical and histopathological features of the tumor are discussed in light of the current literature on MRT at other sites. The bleak prognosis at this site appears to be no different from others - the child succumbed at 10 months old despite surgical resection and initial excellent response to chemotherapy.

CONCLUSION: Malignant rhabdoid tumor has a very poor prognosis and needs to be considered in the differential diagnosis of similar lesions by clinicians involved in pediatric head and neck care.

Original languageEnglish
Pages (from-to)e258-60
JournalJournal of Cranio-Maxillofacial Surgery
Volume40
Issue number8
DOIs
Publication statusPublished - Dec 2012

Bibliographical note

Copyright © 2011 European Association for Cranio-Maxillo-Facial Surgery. Published by Elsevier Ltd. All rights reserved.

Keywords

  • Brain Neoplasms
  • Diagnosis, Differential
  • Fatal Outcome
  • Female
  • Head and Neck Neoplasms
  • Hemangioma
  • Humans
  • Infant
  • Neoplasm Recurrence, Local
  • Rhabdoid Tumor
  • Scalp
  • Skin Neoplasms
  • Teratoma

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