Echocardiographic Screening for Pulmonary Hypertension in Congenital Heart Disease: JACC Review Topic of the Week

CHAMPION Steering Committee

Research output: Contribution to journalReview article (Academic Journal)peer-review

13 Citations (Scopus)

Abstract

Echocardiography is the mainstay in screening for pulmonary hypertension (PH). International guidelines suggest echocardiographic parameters for suspecting PH, but these may not apply to many adults with congenital heart disease (ACHD). PH is relatively common in ACHD patients and can significantly affect their exercise capacity, quality of life, and prognosis. Identification of patients who have developed PH and who may benefit from further investigations (including cardiac catheterization) and treatment is thus extremely important. A systematic review and survey of experts from the United Kingdom and Ireland were performed to assess current knowledge and practice on echocardiographic screening for PH in ACHD. This paper presents the findings of the review and expert statements on the optimal approaches when using echocardiography to assess ACHD patients for PH, with particular focus on major subgroups: patients with right ventricular outflow tract obstruction, patients with systemic right ventricles, patients with unrepaired univentricular circulation, and patients with tetralogy of Fallot with pulmonary atresia.

Original languageEnglish
Pages (from-to)2778-2788
Number of pages11
JournalJournal of the American College of Cardiology
Volume72
Issue number22
DOIs
Publication statusPublished - 4 Dec 2018

Bibliographical note

Copyright © 2018 The Authors. Published by Elsevier Inc. All rights reserved.

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