Abstract
Rhomboencephalitis—inflammation of the brainstem and cerebellum—has myriad clinical presentations including encephalopathy, cranial neuropathies, long tract signs and cerebellar dysfunction and is associated with significant morbidity and mortality. There are a variety of potential underlying causes that respond variably to treatment, including infections, parainfective syndromes, inflammatory disorders including autoimmune encephalitis and paraneoplastic syndromes. Here, we review its clinical presentation and outline a practical approach to its investigation, aiming to facilitate prompt diagnosis and confirmation of the underlying cause, to start appropriate management early and optimise the clinical outcome.
Original language | English |
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Article number | 002680 |
Pages (from-to) | 108-118 |
Number of pages | 11 |
Journal | Practical Neurology |
Volume | 21 |
Issue number | 2 |
Early online date | 8 Dec 2020 |
DOIs | |
Publication status | Published - 16 Mar 2021 |