Jonathan Cleaver, Richard James, Claire M Rice*

*Corresponding author for this work

Research output: Contribution to journalReview article (Academic Journal)peer-review

3 Citations (Scopus)
504 Downloads (Pure)


Rhomboencephalitis—inflammation of the brainstem and cerebellum—has myriad clinical presentations including encephalopathy, cranial neuropathies, long tract signs and cerebellar dysfunction and is associated with significant morbidity and mortality. There are a variety of potential underlying causes that respond variably to treatment, including infections, parainfective syndromes, inflammatory disorders including autoimmune encephalitis and paraneoplastic syndromes. Here, we review its clinical presentation and outline a practical approach to its investigation, aiming to facilitate prompt diagnosis and confirmation of the underlying cause, to start appropriate management early and optimise the clinical outcome.
Original languageEnglish
Article number002680
Pages (from-to)108-118
Number of pages11
JournalPractical Neurology
Issue number2
Early online date8 Dec 2020
Publication statusPublished - 16 Mar 2021


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